Ư (idiopathic epilepsy) ̴. ð ̿ Ű ̻ Ÿ ʰ Ȱ ϴ Ư¡̴. ڽ ֿϵ Ÿ ȣڴ ǰ, ã ȴ.
ϸ Ű Ÿ ʱ ȣڴ ǥ, ǻ ̻Ұ 찡 . ܼ ǽ Ͽٰ Ͼ 쿡 ǽ(syncope) (narcolepsy/cataplexy) ϱ 쵵 ִ. ȯ ϱ ؼ ӻ ߿ϰ, Ż ſ ߿ Ѵ. Ư ϱ ؼ ΰ ȯ(缺 ȯ,) ΰ ȯ(, ) ؾ Ѵ.
⺻ װ˻ ˻, 缱 ˻縦 ؼ ΰ ȯ ִ. ΰ ȯ ϱ ؼ CT Ǵ MRI Կ ô ˻簡 ʿϴ. İ˻絵 ʿ, п , ӻ Ȱǰ ʴ. ʴ Ư ܵǾ, װ ȭ Į(potassium brimde; KBr) ܵ Ͽ Ǿ.
ֵ 2 Ǫ
3 ̴Ͼ Ǫ ְ ֵ ߴ. ۽ Ͽ, (tonic) ǽ 财 ߴ. ý Ⱦڼ (pedaling) Ǿ. 2~5 ӵǾ, 3 . ȯ ǽ ̾, Ű ˻翡 Ư . ü 39.7ɷ , ٸ Ȱ¡(vital sign) ̾.
ӻ ¸ Ư , ȯ Ȯϱ , װ û ȭа˻, ˻, 缱˻, İ˻, ˻ ǽߴ.
ûȭа˻翡 AST CK(CPK) ̾ Ǿ. ̴ ȴ. ܿ ̻ . ˻翡 Ư . ι缱 Կ ̾ Ұ(microhepatia) Ǿ. İ˻ ˻絵 ̾. װ˻翡 ˺ι, ݷ, ߿, , (MCV) ̾Ƿ Ұ üȯƮ(portosystemic shunt;PSS) ǽϱ ٰŰ ʹ ̾ߴ. ̸ ϱ ˻縦 ǽߴ.
˻翡 ̻ . ̻ ˻ ΰ ȯ Ǿ. 2 ٽ Ǿ ڱ(magnetic response image; MRI)Կ ô ˻縦 ߴ. MRI Կ ¿ ̾ Ī Ǿ, ۿ Ư . ô (cisterna magna) õ, õڵ ô ߴ. ܹ 15mg/dl , ټ(total nuclear cell count; TNCC) 0cells/l̾, ˻翡 ʾҴ. ߰˻翡 ΰ Ȯ .
° ü˻, Ű ˻, ӻ ˻, 缱 ˻ ̾, MRIԿ ôװ˻翡 ̾. Ư ߴ. Ư ¸ ϱ ؼ İ˻縦 ǽؾ , ʿ ǽ ʾҴ.
ÿ , ˻縦 ϴ ȿ Ǿ. 3 ӵǾ, ǽ , (pedaling) ̾. װ ʱ KBr óߴ. 250mg/ml KBr 100ml ó߰, Ϸ 1 40mg/kg(0.72ml) Բ Կ. Bromide Cl ؼ 輳DZ § ﰡ Ѵ. 3° Bromide ϱ ؼ Antech Diagnostics û ´. û 0.8mg/ml ġ Ǿ. ġ ġ 1.0mg/ml ̰, ؾ ϴ KBr Ŀ ؼ ϸ 50mg/kg(0.9ml)̴. Ŀ Ϸ翡 1 0.9ml Բ ߴ. ߱ 3 ٽ ؾ ϴµ, ȣ ߾. , KBr ġḦ ϰ 1° 2 Ǿ.
ñ KBr ϱ ñ̴. KBrġ Ͽ ߴٰ Ǵ߰, KBr ġ ϱ ؼ ð ʿϹǷ ٺŻ(phenobarbital: PB) Բ ϱ ߴ.
PB 2.5mg/kg Ϸ翡 2ȸ 汸ߴ. ߳ ʹ ߰, KBr ġ ϰ, PB ̾. Bromide ġ 2° ٽ ǽߴ. ߳ 1.3mg/ml ġ ġ Ҵ. Bromide 2 ˻ 1ȸ ߰ ߴ. 20 . 2 Ŀ ߴ.
Ŀ ʾҴ. PB(2.5mg/kg, bid) KBr(50mg/kg, sid) 7 Բ ߴ. ġ ʱ 1ȸ Ǿ, Ŀ ʾҴ. ġ 7° PB ߰, KBr Ͽ. 6 Bromide ߳ Ͽµ, 2.2mg/ml Ǿ. 17 ʾҴ.
ʴ Ƚ װ ġᰡ ʿϴ. װ ó , ؾ ϰ, ̸ ȣڰ ϰ ־ Ѵ. ߿ װ ٽ Ÿ ִ.
κ ȣڵ 1 װ Ѵ. 1 ϸ Ƿ װ ó ̷ ȴ. ٰ ϸ ٽ ó Ѵ. Ƚ ٸ ɼ Ƿ ؾ ȣڿ Ѿ Ѵ.